PT  - JOURNAL ARTICLE
AU  - Nandhagopal, Ramachandiran
AU  - Al-Murshedi, Fathiya
AU  - Al-Busaidi, Mujahid
AU  - Al-Busaidi, Amna
TI  - Encephalopathy mimicking non-convulsive status Epilepticus
AID  - 10.17712/nsj.2018.1.20170214
DP  - 2018 Jan 01
TA  - Neurosciences Journal
PG  - 52--56
VI  - 23
IP  - 1
4099  - http://nsj.org.sa/content/23/1/52.short
4100  - http://nsj.org.sa/content/23/1/52.full
SO  - Neurosciences (Riyadh)2018 Jan 01; 23
AB  - Primary hyperammonemic encephalopathy due to urea cycle disorders (UCD) typically manifests with episodic unresponsiveness and this clinical entity is not often included in the differential diagnosis of presumed non-convulsive status epilepticus (NCSE). However, this diagnostic consideration has therapeutic implications. In this report, we document the therapeutic importance of elucidating the specific cause of hyperammonemic encephalopathy that closely mimicked NCSE through 2 unique illustrative cases.