RT Journal Article
SR Electronic
T1 Encephalopathy mimicking non-convulsive status Epilepticus
JF Neurosciences Journal
JO Neurosciences (Riyadh)
FD Prince Sultan Military Medical City
SP 52
OP 56
DO 10.17712/nsj.2018.1.20170214
VO 23
IS 1
A1 Nandhagopal, Ramachandiran
A1 Al-Murshedi, Fathiya
A1 Al-Busaidi, Mujahid
A1 Al-Busaidi, Amna
YR 2018
UL http://nsj.org.sa/content/23/1/52.abstract
AB Primary hyperammonemic encephalopathy due to urea cycle disorders (UCD) typically manifests with episodic unresponsiveness and this clinical entity is not often included in the differential diagnosis of presumed non-convulsive status epilepticus (NCSE). However, this diagnostic consideration has therapeutic implications. In this report, we document the therapeutic importance of elucidating the specific cause of hyperammonemic encephalopathy that closely mimicked NCSE through 2 unique illustrative cases.