RT Journal Article SR Electronic T1 Rosette-Forming Glioneural tumor of the fourth ventricle JF Neurosciences Journal JO Neurosciences (Riyadh) FD Prince Sultan Military Medical City SP 284 OP 288 DO 10.17712/nsj.2021.3.20200163 VO 26 IS 3 A1 Sarah A. Bin Abdulqader A1 Salwa Al-Shibani A1 Wafa Alshawakeer A1 Gmaan Alzhrani YR 2021 UL http://nsj.org.sa/content/26/3/284.abstract AB Rosette-forming glioneural tumors (RGNTs) are rare. Here, we report a case of RGNT of the fourth ventricle in an 18-year-old female. The patient presented with a 4-month history of headache and dizziness. Neurological examination showed papilledema, impaired tandem gait, and right-sided dysmetria. Radiological images showed a posterior fossa lesion in the fourth ventricle with hydrocephalus. An emergent ventriculostomy was performed followed by gross total surgical resection of the lesion. Histopathological examination confirmed the diagnosis of RGNT. The patient developed posterior fossa syndrome postoperatively which improved on follow-up. Although rare, RGNT should be considered in the differential diagnoses of posterior fossa lesions in young patients. Given its benign course, surgical resection remains the treatment of choice.