Table 1

Common clinical manifestations of PACNS.

Adult PACNS*
 Headache
 Cognitive dysfunction
 Hemiparesis
 Consistent neurologic deficit or stroke
 Visual symptoms
 Transient ischemic attack
 Aphasia
 Seizures
 Ataxia
 Intracranial hemorrhage
Large-medium vessel cPACNS
 Focal neurologic deficits
  1. Acute hemiparesis
  2. Hemisensory loss
  3. Fine motor skill loss
  4. Hemifacial weakness
 Headaches
 Seizures
 Diffuse neurologic deficit
Small-vessel cPACNS
 Any neurologic or psychiatric symptoms
  • * PACNS - primary angiitis of the central nervous system,

  • cPACNS - children primary angiitis of the central nervous system