Summary of published cases of brainstem angiocentric gliomas. M: male, F:female, CN: cranial nerve, ETV: endoscopic third ventriculostomy, NTR: near total resection, VPS: ventriculoperitoneal shunt.
| No. | Author (year) | Age (gender) | Location | Presentation/exam | Surgery | Chemotherapy | Follow up | Outcome | MYB-QKI fusion |
|---|---|---|---|---|---|---|---|---|---|
| 1 | Covington et al (2009) | 5 years (F) | Right exophytic tectal lesion | Unsteady gait, 4th and 7th CN palsies, hydrocephalus | ETV, craniotomy and debulking | No | 2 years | Stable lesion | Yes |
| 2 | Weaver et al (2017) | 5 years (F) | Midline midbrain tegmentam | Diplopia, 6th CN nerve palsy, hydrocephalus | ETV, craniotomy and NTR | NO | 6 years | Stable after resection | No data |
| 3 | Weaver et al (2017) | 6 years (M) | Right pontine exophytic lesion | Hemiparesis, facial palsy | Stereotactic biopsy and ETV | No | 1.5 years | Stable lesion | No data |
| 4 | D’Aronco et al (2017) | 7 years (M) | Pontomedullary exophytic lesion | respiratory failure, repated pneumonia | Stereotactic biopsy | Yes (carboplatin/vincristine) | 10 months | Progression | Yes |
| 5 | D’Aronco et al (2017) | 3 years (F) | Pontomedullary exophytic lesion | Facial palsy | Stereotactic biopsy | Yes (vinblastine and bevacizumab) | 4 years | Progression | Yes |
| 6 | Chan et al (2017) | 7 Years (M) | Pons | 6th CN palsy | Stereotactic biopsy | No data | No data | No data | Yes |
| 7 | Current case (2019) | 4 years (F) | Left brainstem dorsal exophytic lesion | Hydrocephalus, unsteady gait, hoarseness, choking with food, 6th,7th, and lower CN palsies | Craniotomy and debulking, VPS | Yes (carboplatin/vincristine) | 8 years | Progression | Not done |