Objectives: To explore therapeutic attitude of healthcare providers practicing in pediatric
critical care in Saudi Arabia toward patients with Spinal Muscular Atroph (SMA) Type I, and …

Spinal muscular atrophy (SMA) is a neuromuscular disorder characterized by muscle
atrophy and severe proximal muscle weakness. In the absence of curative treatment, it has …

Background: Patients with spinal muscular atrophy (SMA) have compromised respiratory
muscle function which results in impaired cough, hypoventilation during sleep, and chest …

Background: Without ventilatory support, premature death from respiratory insufficiency is
virtually universal in infants with spinal muscular atrophy type 1 (SMA1). With mechanical …

Background: Spinal muscular atrophy (SMA) is a neurodegenerative disease that results in
progressive muscular atrophy and weakness. The primary cause of morbidity and mortality …

Objective. To determine whether there is variability in the attitudes and practices of
physicians regarding treatment of respiratory failure in children with spinal muscular atrophy …

Objectives: To determine physicians' attitudes and stated practice in the management of
patients with spinal muscular atrophy (SMA). We also aimed to explore their knowledge …

The authors wish to thank the editors for the opportunity to respond to Bach et al. The
authors are unclear why there would be a lack of clarity regarding our noninvasive …

PURPOSE: The ethics of invasive mechanical ventilation for children with the progressive
neuromuscular disease Spinal Muscular Atrophy Type I (SMA I) is highly debated. We …

Introduction ultimately death during infancy from chronic respiratory failure. There is
considerable debate regarding the ethics of invasive mechanical ventilation for SMA I …