Skip to main content

Main menu

  • Home
  • Content
    • Latest
    • Ahead of print
    • Archive
  • Info for
    • Authors
    • Reviewers
    • Subscribers
    • Institutions
    • Advertisers
  • About Us
    • About Us
    • Editorial Office
    • Editorial Board
  • More
    • Alerts
    • Feedback
    • Folders
    • Help
  • Other Publications
    • Saudi Medical Journal

User menu

  • My alerts
  • Log in

Search

  • Advanced search
Neurosciences Journal
  • Other Publications
    • Saudi Medical Journal
  • My alerts
  • Log in
Neurosciences Journal

Advanced Search

  • Home
  • Content
    • Latest
    • Ahead of print
    • Archive
  • Info for
    • Authors
    • Reviewers
    • Subscribers
    • Institutions
    • Advertisers
  • About Us
    • About Us
    • Editorial Office
    • Editorial Board
  • More
    • Alerts
    • Feedback
    • Folders
    • Help
  • Follow psmmc on Twitter
  • Visit psmmc on Facebook
  • RSS
Case ReportCASE REPORTS
Open Access

Susac syndrome. A differential diagnosis for demyelination

Surjith Vattoth, Christopher J. Compton, Glenn H. Roberson and Michael S. Vaphiades
Neurosciences Journal January 2013, 18 (1) 74-78;
Surjith Vattoth
Department of Radiology, Neuroradiology Section, University of Alabama at Birmingham, 619 19th Street South, Birmingham, Alabama 35249-6830, United States of America. Tel. +1 (205) 9343920. Fax. +1 (205) 9759262. E-mail: [email protected]
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
  • For correspondence: [email protected]
Christopher J. Compton
Department of Radiology, Neuroradiology Section, University of Alabama at Birmingham, 619 19th Street South, Birmingham, Alabama 35249-6830, United States of America. Tel. +1 (205) 9343920. Fax. +1 (205) 9759262. E-mail: [email protected]
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
  • For correspondence: [email protected]
Glenn H. Roberson
Department of Radiology, Neuroradiology Section, University of Alabama at Birmingham, 619 19th Street South, Birmingham, Alabama 35249-6830, United States of America. Tel. +1 (205) 9343920. Fax. +1 (205) 9759262. E-mail: [email protected]
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
  • For correspondence: [email protected]
Michael S. Vaphiades
Department of Radiology, Neuroradiology Section, University of Alabama at Birmingham, 619 19th Street South, Birmingham, Alabama 35249-6830, United States of America. Tel. +1 (205) 9343920. Fax. +1 (205) 9759262. E-mail: [email protected]
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
  • For correspondence: [email protected]
  • Article
  • eLetters
  • Info & Metrics
  • PDF
Loading

Abstract

Susac syndrome is a microangiopathy of unknown origin, probably autoimmune, affecting capillaries and precapillary arterioles of the brain, retina, and inner ear. It is often misdiagnosed as acute disseminated encephalomyelitis or multiple sclerosis. We report the case of a 25-year-old male with Susac syndrome who developed the clinical triad of encephalopathy, visual and hearing problems over the course of a year. The characteristic MRI findings including central corpus callosal involvement and brain infarctions were supported by branch retinal arterial/arteriolar occlusions on fluorescein retinal angiography. Most patients with Susac syndrome will not have the complete clinical triad initially. A very high index of suspicion is required by the clinician and radiologist in patients with any component of the clinical triad so as not to misdiagnose the MRI findings for demyelination. Even if initial ophthalmologic examinations are normal, these patients should be followed up for later development of branch retinal artery occlusions.

  • Copyright: © Neurosciences

Neurosciences is an Open Access journal and articles published are distributed under the terms of the Creative Commons Attribution-NonCommercial License (CC BY-NC). Readers may copy, distribute, and display the work for non-commercial purposes with the proper citation of the original work.

PreviousNext
Back to top

In this issue

Neurosciences Journal: 18 (1)
Neurosciences Journal
Vol. 18, Issue 1
1 Jan 2013
  • Table of Contents
  • Cover (PDF)
  • Index by author
Download PDF
Email Article

Thank you for your interest in spreading the word on Neurosciences Journal.

NOTE: We only request your email address so that the person you are recommending the page to knows that you wanted them to see it, and that it is not junk mail. We do not capture any email address.

Enter multiple addresses on separate lines or separate them with commas.
Susac syndrome. A differential diagnosis for demyelination
(Your Name) has sent you a message from Neurosciences Journal
(Your Name) thought you would like to see the Neurosciences Journal web site.
Citation Tools
Susac syndrome. A differential diagnosis for demyelination
Surjith Vattoth, Christopher J. Compton, Glenn H. Roberson, Michael S. Vaphiades
Neurosciences Journal Jan 2013, 18 (1) 74-78;

Citation Manager Formats

  • BibTeX
  • Bookends
  • EasyBib
  • EndNote (tagged)
  • EndNote 8 (xml)
  • Medlars
  • Mendeley
  • Papers
  • RefWorks Tagged
  • Ref Manager
  • RIS
  • Zotero
Share
Susac syndrome. A differential diagnosis for demyelination
Surjith Vattoth, Christopher J. Compton, Glenn H. Roberson, Michael S. Vaphiades
Neurosciences Journal Jan 2013, 18 (1) 74-78;
Twitter logo Facebook logo Mendeley logo
  • Tweet Widget
  • Facebook Like
  • Google Plus One
Bookmark this article

Jump to section

  • Article
  • eLetters
  • Info & Metrics
  • PDF

Related Articles

  • No related articles found.
  • Google Scholar

Cited By...

  • No citing articles found.
  • Google Scholar

More in this TOC Section

  • A novel variant of RBCK1 gene causes mild polyglucosan myopathy
  • Unusual presentation of neurobrucellosis in Jeddah, Kingdom of Saudi Arabia
  • Sjogren’s syndrome associated with bilateral peripheral facial paralysis
Show more CASE REPORTS

Similar Articles

Navigate

  • home

More Information

  • Help

Additional journals

  • All Topics

Other Services

  • About

© 2025 Neurosciences Journal Neurosciences is copyright under the Berne Convention and the International Copyright Convention. All rights reserved. Neurosciences is an Open Access journal and articles published are distributed under the terms of the Creative Commons Attribution-NonCommercial License (CC BY-NC). Readers may copy, distribute, and display the work for non-commercial purposes with the proper citation of the original work. Electronic ISSN 1658-3183. Print ISSN 1319-6138.

Powered by HighWire